Pulmonary Artery Agenesis with Bronchial Asthma

Document Type: Case Report

Authors

1 Pulmonologist, Faculty of Medicine, Ardabil University of Medical Sciences, Ardabil, Iran

2 Internist, Emam Khomeini Hospital, Ardabil University of Medical Sciences, Ardabil, Iran

Abstract

Unilateral Pulmonary Artery Agenesis (UPAA) is a rare congenital anomaly during the 4 th  week of gestational age. It is defined as an absence of pulmonary parenchyma and its supporting artery. A 9-year-old girl was admitted to our hospital because of chronic cough. Chest examination showed a decrement in lung sound of right hemi-thorax with expiratory wheeze. Chest radiography (CXR) revealed a semi-opaque right hemi-thorax. Chest CT with intra-venous contrast demonstrated absence of the right pulmonary artery and lung parenchyma with hyper-inflated left lung and dextro-position of mediastinum. This case emphasizes that in patients with respiratory compliant and chronic cough CXR must be done to rule out similar diagnosis other than asthma.
 
 

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