Cystic Lung Disease in a Young man

Document Type : Image in Cardio-Thoracic Medicine


1 Thoracic Surgeon, Lung Disease Research Center, Mashhad University of Medical Sciences, Mashhad, Iran.

2 Pulmonologist, Lung Disease Research Center, School of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran


A 32-year-old man was admitted in the Emergency Department with acute dyspnea secondary to spontaneous pneumothorax. He had history of spontaneous pneumothorax 2 years ago.
He was active cigarette smoker (10 pack/year). The family history was unremarkable for lung diseases. Additionally, he had no systemic complaints.
The lung HRCT revealed multiple bizarre-shaped cysts distributed in both lungs with more severe involvement of upper and middle parts (Figure 1).
Since the HRCT findings were characteristic and he was smoker, the diagnosis of pulmonary langerhans cell histiocytosis (PLCH) was proposed. Small chest tube was inserted in left side and after 5 days it was easily removed.
He was recommended to quit smoking and close follow-up.