Cor Triatriatum Sinistrum Presenting as Cyanotic Congenital Heart Disease A Rare Case Report

Document Type : Case Report

Authors

1 Cardiologist, Department of Cardiology, J.L.N. Hospital , Ajmer, Rajasthan, India

2 Resident of Cardiology, Department of Cardiology, J.L.N. Hospital , Ajmer, Rajasthan,India

3 Resident of Cardiology, Department of Cardiology, J.L.N. hospital , Ajmer, Rajasthan, India

4 Resident of Cardiology, Department of Cardiology, J.L.N. Hospital , Ajmer, Rajasthan, India

Abstract

 
Cor triatriatum is an acyanotic congenital heart disease. We present a rare case of cor triatriatum sinistrum in a 6-month-old female infant who was presented with cyanosis and failure to thrive. The 2D transthoracic echocardiography and the Doppler color flow imaging showed a proximal venous chamber communicating to the distal left atrium  through restrictive opening to the low-pressure, distal left atrial chamber.
The Saline Contrast Echocardiography confirmed a right-to-left atrial shunt due to a minor atrial septal defect. The defect was caused by a persistent pulmonary hypertension which had raised the right atrial pressure in the infant.
To the best of our knowledge, barely any such cases have been reported in the literature so far. Our report highlights the clinical utility of the Saline Contrast Echo in other cases of congenital heart diseases.

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References

1.Krabil KA, Lucas RV Jr. Abnormal pulmonary connections, Moss and Adams Heart Disease in infants, children and Adolescents including the fetus and young adult. 5th ed. Vol. 1, Philadelphia, Lippinkott William and Wilkins, 1995. p. 863-8.
2.Jacobstein MD, Hirschfeld SS. Concealed left atrial membrane: pitfalls in the diagnosis of cor triatriatum and supravalve mitral ring. Am J Cardiol 1982;49:780-786.
3.Van Praagh R, Corsini I. Cor triatriatum: Pathologic anatomy and a consideration of morphogenesis based on 13 postmortem cases and a study of normal development of the pulmonary vein and atrial septum in 83 human embryos. Am Heart J 1969;78:379-388.
4. Kerensky RA, Bertolet BD, Epstein M. Late discovery of cor triatriatum as a result of unilateral pulmonary venous obstruction. Am Heart J 1995;130:624-627.
5.Gonzalez-Juanatey C, Testa A, Vidan J, Izquierdo R, Garcia-Castelo A, Daniel C, Armesto V. Persistent left superior vena cava draining into the coronary sinus: report of 10 cases and literature review. Clin Cardiol 2004; 27: 515–518.
6.Mc Lean MK, Kung GC, Polimenakos A, Wells WJ, Reemtsen BL. Cor triatriatum associated with ASD and common atrium in 7-month-old with tachypnea and failure to thrive. Ann Thorac Surg 2008;86:1999. 
Journal of Cardio-Thoracic Medicine
Volume 3, Issue 1 - Serial Number 1
January 2015
Pages 278-280

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