Journal of Cardio-Thoracic Medicine

Journal of Cardio-Thoracic Medicine

Apical Hypertrophic Cardiomyopathy in a Case with Chest Pain and Family History of Sudden Cardiac Death: A Case Report

Document Type : Case Report

Authors
Mostafa Ahmadi
Ramin Khameneh Bagheri
Cardiologist, Division of Cardiovascular, Vascular Surgery Research Center, Mashhad University of Medical Sciences, Mashhad, Iran
10.22038/jctm.2017.25214.1137
Abstract
Hypertrophic cardiomyopathy (HCM) is the most common genetic cardiovascular disease, which is caused by a multitude of mutations in genes encoding proteins of the cardiac sarcomere (1). Apical hypertrophic cardiomyopathy (AHCM) is an uncommon type of HCM. The sudden cardiac death is less likely to occur in the patients inflicted with AHCM (2). Herein, we presented the case of a 29-year-old man with AHCM, who had typical exertional chest pain without any cardiovascular risk factors, except for a sudden cardiac death in his older brother at the age of 28 years. After performing complete clinical and paraclinical evaluations, the patient underwent optimal medical treatment with beta-blocker agents without any symptoms.
Keywords
AHCM
Family history
Sudden cardiac death
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Journal of Cardio-Thoracic Medicine
Volume 5, Issue 3
Summer 2017
Pages 198-200